Cardiopulmonary involvement in Fabry's disease

: Koskenvuo JW, Kantola IM, Nuutila P, Knuuti J, Parkkola R, Mononen I, Hurme S, Kalliokoski R, Viikari JS, Wendelin-Saarenhovi M, Kiviniemi TO, Hartiala JJ

Publisher: ACTA CARDIOLOGICA

: 2010

: Acta Cardiologica

: ACTA CARDIOLOGICA

: ACTA CARDIOL

: 2

: 65

: 2

: 185

: 192

: 8

: 0001-5385

DOI: https://doi.org/10.2143/AC.65.2.2047052

Conclusion - LVH and reduced exercise capacity are the most apparent cardiopulmonary changes in Fabry's disease but they have only a minor association to cardiopulmonary symptoms. Therefore, routine cardiopulmonary evaluation in Fabry's disease using echocardiography is maybe enough when integrated to counselling for aerobic exercise training.