A1 Refereed original research article in a scientific journal
Cardiopulmonary involvement in Fabry's disease
Authors: Koskenvuo JW, Kantola IM, Nuutila P, Knuuti J, Parkkola R, Mononen I, Hurme S, Kalliokoski R, Viikari JS, Wendelin-Saarenhovi M, Kiviniemi TO, Hartiala JJ
Publisher: ACTA CARDIOLOGICA
Publication year: 2010
Journal: Acta Cardiologica
Journal name in source: ACTA CARDIOLOGICA
Journal acronym: ACTA CARDIOL
Number in series: 2
Volume: 65
Issue: 2
First page : 185
Last page: 192
Number of pages: 8
ISSN: 0001-5385
DOI: https://doi.org/10.2143/AC.65.2.2047052
Abstract
Conclusion - LVH and reduced exercise capacity are the most apparent cardiopulmonary changes in Fabry's disease but they have only a minor association to cardiopulmonary symptoms. Therefore, routine cardiopulmonary evaluation in Fabry's disease using echocardiography is maybe enough when integrated to counselling for aerobic exercise training.
Conclusion - LVH and reduced exercise capacity are the most apparent cardiopulmonary changes in Fabry's disease but they have only a minor association to cardiopulmonary symptoms. Therefore, routine cardiopulmonary evaluation in Fabry's disease using echocardiography is maybe enough when integrated to counselling for aerobic exercise training.