A1 Refereed original research article in a scientific journal
Klippel-Trenaunay Syndrome Manifesting as Gingival Overgrowth and Teeth Agenesis
Authors: Ozdemir H, Marakoglu I, Akyol M, Goze OF, Gursoy UK
Publisher: JOURNAL PEDODONTICS INC
Publication year: 2010
Journal: Journal of Clinical Pediatric Dentistry
Journal name in source: JOURNAL OF CLINICAL PEDIATRIC DENTISTRY
Journal acronym: J CLIN PEDIATR DENT
Volume: 34
Issue: 4
First page : 351
Last page: 354
Number of pages: 4
ISSN: 1053-4628
DOI: https://doi.org/10.17796/jcpd.34.4.l41414372l4332m1
Abstract
Objective: Klippel-Trenaunay syndrome (KTS) is characterized by triad of venous varicosity, naevus flammeus, and soft/hard tissue hypertrophy. Manifestations of the syndrome in the head and neck region are rare, but in some cases hemangioma of the lips, tongue, and gums, open bite and cross bite, and early tooth eruption are associated with the disease. Study design: We report a 12-year-old KTS patient with gingival hyperplasia, congenital missing teeth, and increased mucosal vascularization as oral manifestations. Results and conclusion: All manifestations of the KTS were observed on the same side of the head, except bilateral missing teeth. Histological examination showed several vascular enlargements in enlarged gingiva. It is suggested that oral manifestations of the syndrome are generally related to the severity of the disease, but they do not always present in the same pattern.
Objective: Klippel-Trenaunay syndrome (KTS) is characterized by triad of venous varicosity, naevus flammeus, and soft/hard tissue hypertrophy. Manifestations of the syndrome in the head and neck region are rare, but in some cases hemangioma of the lips, tongue, and gums, open bite and cross bite, and early tooth eruption are associated with the disease. Study design: We report a 12-year-old KTS patient with gingival hyperplasia, congenital missing teeth, and increased mucosal vascularization as oral manifestations. Results and conclusion: All manifestations of the KTS were observed on the same side of the head, except bilateral missing teeth. Histological examination showed several vascular enlargements in enlarged gingiva. It is suggested that oral manifestations of the syndrome are generally related to the severity of the disease, but they do not always present in the same pattern.
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