A1 Refereed original research article in a scientific journal
Lung function in diastrophic dysplasia
Authors: Remes V, Helenius I, Peltonen J, Poussa M, Sovijarvi A
Publisher: WILEY-LISS
Publication year: 2002
Journal:: Pediatric Pulmonology
Journal name in source: PEDIATRIC PULMONOLOGY
Journal acronym: PEDIATR PULM
Volume: 33
Issue: 4
First page : 277
Last page: 282
Number of pages: 6
ISSN: 8755-6863
DOI: https://doi.org/10.1002/ppul.10069
Abstract
Although the patients with DD had, on average, normal lung volumes, large individual variation occurred. Airway resistance was increased in adults. The angle of scoliosis correlated inversely with lung volume parameters. (C) 2002 Wiley-Liss. Inc.