A1 Vertaisarvioitu alkuperäisartikkeli tieteellisessä lehdessä
Comprehensive multi-modality imaging approach in arrhythmogenic cardiomyopathy—an expert consensus document of the European Association of Cardiovascular Imaging
Tekijät: Kristina H. Haugaa, Cristina Basso, Luigi P. Badano, Chiara Bucciarelli-Ducci, Nuno Cardim, Oliver Gaemperli, Maurizio Galderisi, Gilbert Habib, Juhani Knuuti, Patrizio Lancellotti, William McKenna, Danilo Neglia, Bogdan A. Popescu, Thor Edvardsen
Kustantaja: OXFORD UNIV PRESS
Julkaisuvuosi: 2017
Lehti:EHJ Cardiovascular Imaging / European Heart Journal - Cardiovascular Imaging
Tietokannassa oleva lehden nimiEUROPEAN HEART JOURNAL-CARDIOVASCULAR IMAGING
Lehden akronyymi: EUR HEART J-CARD IMG
Vuosikerta: 18
Numero: 3
Aloitussivu: 237
Lopetussivu: 253
Sivujen määrä: 17
ISSN: 2047-2404
eISSN: 2047-2412
DOI: https://doi.org/10.1093/ehjci/jew229
Arrhythmogenic cardiomyopathy (AC) is a progressive disease with high risk of life-threatening ventricular arrhythmias. A genetic mutation is found in up to 50-60% of probands, mostly affecting desmosomal genes. Diagnosis of AC is made by a combination of data from different modalities including imaging, electrocardiogram, Holter monitoring, family history, genetic testing, and tissue properties. Being a progressive cardiomyopathy, repeated cardiac imaging is needed in AC patients. Repeated imaging is important also for risk assessment of ventricular arrhythmias. This expert consensus document gives clinical recommendations for how to use multi-modality imaging in the different aspects of AC disease, including diagnosis, family screening, follow-up, risk assessment, and differential diagnosis.
